Thoracoabdominal ectopia cordis is better known as the pentalogy of Cantrell and is in part a misnomer, given that the heart is not truly ectopic.
In pentalogy of Cantrell the heart is abnormally sited with the apex oriented down, but is positioned within the chest and therefore not ectopia cordis. Both cervical and abdominal ectopia cordis may occur without a sternal cleft. Abdominal ectopia cordis does not belong in this group of anomalies because the defect is diaphragmatic and does not involve the thorax or the anterior abdominal wall.
No comments:
Post a Comment